© 2020 by Pediatric Infectious Diseases and Immunization Society.Objective: Hydatid disease, caused by the Echinococcus species, is a zoonotic disease seen in the rural areas of the world. Although it is generally acquired in chilhood, pediatric reports are limited. Herein, we aimed to evaluate the demographic data and clinical process of children diagnosed with hydatid disease, which is still a widespread and important public health problem in our country. Material and Methods: The medical records of patients hospitalized with the diagnosis of hydatid disease between June 2015 and August 2019 were evaluated retrospectively. Results: There were a total of 56 patients, with 26 females and 30 males. Their median age was 10.25 (2.75-17.5) years. Liver was the most frequently affected organ (55.4%), followed by lungs (39.1%), spleen (3.6%), cardiac (1.8%) and renal (1.8%). The median size of the cysts in total was 6.0 (1-12) cm. Seven patients had multicystic involvement. Twelve patients developed rupture of cysts. The patients who developed rupture had more symptoms of cough and fatigue and cysts larger than 5 cm. Five patients had bronchial expansion, four patients developed secondary abscess formation, and three patients developed rupture of cyst to the bile duct. Conclusion: Hydatid disease leads to a significant financial burden in developing countries. Prevention and control programs composed of health and personal habit education must be considered in endemic areas.