Chediak-Higashi syndrome in the intensive care unit


Demirkiran O., Utku T. , Urkmez S., Dikmen Y.

PEDIATRIC ANESTHESIA, cilt.14, ss.685-688, 2004 (SCI İndekslerine Giren Dergi) identifier identifier identifier

Özet

Chediak-Higashi Syndrome is a rare autosomal recessive disease characterized by recurrent infections, giant cytoplasmic granules and oculocutaneous albinism. We describe the clinical and laboratory findings of a patient with Chediak-Higashi syndrome who was diagnosed and treated in the intensive care unit because of bleeding tendency after surgery.