Craniorachischisis With A Variant Of Pentalogy Of Cantrell, With Lung Extrophy

Atis A., Demirayak G., Saglam B., Aksoy F., Sen C.

FETAL AND PEDIATRIC PATHOLOGY, cilt.30, ss.431-436, 2011 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 30 Konu: 6
  • Basım Tarihi: 2011
  • Doi Numarası: 10.3109/15513815.2011.587500
  • Sayfa Sayıları: ss.431-436


A case of cranioraschischisis including incomplete pentalogy of Cantrell (PC) is described. The female fetus had a large omphalocele with evisceration of the heart, left lung, liver, stomach, and intestines accompanying anencephaly, cervical, thoracal lumbar, spina bifida. The fetus had ectopia cordis and diaphragmatic agenesia with an intact sternum. We present a case of a neonate with the stigmata for PC with the exception of a sternal defect. A literature review is also included. Sonographers should check for ventral and dorsal anomalies with PC because they may occur simultaneously.